Ayadi A, Pousse H, Soua H, Baizig I, Sfar M T, Mougenot J F, Rambaud C, Martelli H, Schmitz J
Service de pédiatrie, hôpital universitaire de Mahdia, Tunisie.
Arch Pediatr. 1994 May;1(5):493-6.
Parietal vascular malformations of the intestinal tract are rare and their diagnosis is often difficult.
A 2 year-old boy had suffered from intermittent rectal bleeding since the age of one year. Endoscopic examination showed unspecific congestive changes and biopsy showed features of chronic inflammatory changes in the rectum. Barium enema was normal. The patient was operated on, but surgery failed to find any cause for these hemorrhages. Rectal bleedings recurred, some of them resulting in severe anemia. Two further endoscopic examination were grossly negative as was inferior mesenteric arteriography. Spontaneous rectal prolapsus occurred when the boy was 4 years old. This allowed resection of all the submucosal veins of the anal canal; it was followed by complete cessation of rectal bleeding with a follow-up of 36 months. Histological examination showed several ectasias of the capillaries and veins in the submucosa and muscular layers.
Angiectases can occur in a small part of the intestinal tract, and can escape detection by repeated specialized investigation.
肠道壁血管畸形罕见,其诊断往往困难。
一名2岁男孩自1岁起就间歇性直肠出血。内镜检查显示非特异性充血改变,活检显示直肠有慢性炎症改变特征。钡灌肠正常。患者接受了手术,但手术未能找到出血的任何原因。直肠出血复发,其中一些导致严重贫血。另外两次内镜检查结果均为阴性,肠系膜下动脉造影也是如此。男孩4岁时出现自发性直肠脱垂。这使得能够切除肛管所有黏膜下静脉;随后直肠出血完全停止,随访36个月。组织学检查显示黏膜下层和肌层有多处毛细血管和静脉扩张。
血管扩张可发生在肠道的一小部分,并且可能通过反复的专业检查仍无法被发现。