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天使综合征的沟通发展

Communication development in Angelman's syndrome.

作者信息

Jolleff N, Ryan M M

机构信息

Neurosciences Unit, Wolfson Centre, London.

出版信息

Arch Dis Child. 1993 Jul;69(1):148-50. doi: 10.1136/adc.69.1.148.

DOI:10.1136/adc.69.1.148
PMID:8024300
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1029433/
Abstract

The communication development in 11 children with Angelman's syndrome is described. The clinical observation that these children appear to have a greater ability with receptive rather than expressive language is investigated and these skills assessed using published communication schedules. In addition the understanding and the use of nonverbal communication such as natural gesture was studied. The data collected highlight the fact that these children have developed very few words and have difficulty in using gestural or sign systems. This has implications for speech and language therapists and the children's remedial programmes. Possible future longitudinal studies are suggested.

摘要

本文描述了11名患有天使综合征儿童的沟通发展情况。对这些儿童在接受性语言方面似乎比表达性语言能力更强这一临床观察进行了研究,并使用已发表的沟通量表对这些技能进行了评估。此外,还研究了他们对非语言沟通(如自然手势)的理解和运用。收集到的数据凸显了这些儿童词汇量极少且在使用手势或手语系统方面存在困难这一事实。这对言语和语言治疗师以及儿童的康复计划具有启示意义。文中还提出了未来可能进行的纵向研究建议。

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Spoken language comprehension in children and adults with Angelman Syndrome.言语理解在儿童和成人安格曼综合征。
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