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采用整块切除治疗的睫状体神经鞘瘤。

Schwannoma of the ciliary body treated by block excision.

作者信息

Küchle M, Holbach L, Schlötzer-Schrehardt U, Naumann G O

机构信息

Department of Ophthalmology, University of Erlangen-Nürnberg, Germany.

出版信息

Br J Ophthalmol. 1994 May;78(5):397-400. doi: 10.1136/bjo.78.5.397.

DOI:10.1136/bjo.78.5.397
PMID:8025076
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC504796/
Abstract

A 26-year-old man developed a non-pigmented ciliary body tumour of his right eye. A 7 mm block excision and tectonic corneoscleral graft were performed. The excised tissue was studied using histopathological, immunohistochemical, and electron microscopic techniques. The tumour revealed characteristic features of a Schwann cell neoplasm including Antoni A and B patterns, acid mucopolysaccharides, S-100, and vimentin positivity, and--by electron microscopy--Luse bodies. It was classified as a schwannoma. Although rare, schwannoma should be included in the clinical differential diagnosis of non-pigmented ciliary body tumours. Local excision should be considered to avoid over-treatment by enucleation.

摘要

一名26岁男性右眼出现了一个无色素的睫状体肿瘤。进行了7毫米的肿物切除及角膜巩膜支撑移植术。使用组织病理学、免疫组织化学和电子显微镜技术对切除的组织进行了研究。肿瘤呈现出施万细胞瘤的特征性表现,包括Antoni A和B型结构、酸性黏多糖、S-100及波形蛋白阳性,并且在电子显微镜下可见Luse小体。该肿瘤被归类为神经鞘瘤。尽管神经鞘瘤罕见,但在无色素睫状体肿瘤的临床鉴别诊断中应予以考虑。应考虑局部切除以避免眼球摘除的过度治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/d13732a1cf9d/brjopthal00029-0075-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/8b8ec8911314/brjopthal00029-0073-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/fcc182f566c4/brjopthal00029-0074-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/064f049bb25a/brjopthal00029-0074-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/f233816b3e2c/brjopthal00029-0074-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/1fc84c2706a4/brjopthal00029-0075-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/28fe26fdba41/brjopthal00029-0075-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/d13732a1cf9d/brjopthal00029-0075-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/8b8ec8911314/brjopthal00029-0073-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/fcc182f566c4/brjopthal00029-0074-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/064f049bb25a/brjopthal00029-0074-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/f233816b3e2c/brjopthal00029-0074-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/1fc84c2706a4/brjopthal00029-0075-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/28fe26fdba41/brjopthal00029-0075-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/db8d/504796/d13732a1cf9d/brjopthal00029-0075-c.jpg

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