Carli P M
Laboratoire d'Hématologie, Hôpital du Bocage, Dijon, France.
Nouv Rev Fr Hematol (1978). 1994 Apr;36(2):147-9.
Using the registry of hematopoietic malignancies in Cte d'Or, we studied 48 cases of Polycythemia Vera (PV) diagnosed between 1980 and 1990. The overall age-standardized incidence rates, based on the world population, were 0.7 in men and in women. The mean age was 67.0 years in men and 60.5 in women (NS). The incidence decreased during the eleven years of observation. The overall five-year survival rate was 83% and the corrected rate was 100%. 8% of PV transformed into another myeloproliferative disorder (myelofibrosis) and half of them became acute leukaemias.
利用科多尔省造血系统恶性肿瘤登记处的数据，我们研究了1980年至1990年间确诊的48例真性红细胞增多症（PV）病例。基于世界人口的总体年龄标准化发病率，男性和女性均为0.7。男性的平均年龄为67.0岁，女性为60.5岁（无显著性差异）。在十一年的观察期内发病率有所下降。总体五年生存率为83%，校正后生存率为100%。8%的PV转变为另一种骨髓增殖性疾病（骨髓纤维化），其中一半发展为急性白血病。
