Kotel'nikova G P, Kamova N N, Polianskaia I P
Ter Arkh. 1993;65(5):34-7.
Specific characteristics and localization of histomorphological alterations observed in Bechterew's disease (BD) cause specific features in clinical pattern of the disease. Combined cardiological examination of 49 BD patients revealed in them: valvular disease (6 cases), aortal insufficiency (8.2%), left ventricular dilatation (12%), mitral prolapse (16.3%), aortal dilatation (14%). Two-dimensional echocardiography registered typical subaortic protrusion in 3 out of 30 examinees. At ECG examination of 46 patients atrioventricular block was registered in 4, bundle-branch block in 7, affected conductivity in 10 patients. In complicating amyloidosis one can observe a typical picture of amyloid cardiac infiltration.
在贝赫切特病(BD)中观察到的组织形态学改变的特定特征和定位导致了该疾病临床模式的特定特征。对49例BD患者进行的综合心脏检查发现:瓣膜病(6例)、主动脉瓣关闭不全(8.2%)、左心室扩张(12%)、二尖瓣脱垂(16.3%)、主动脉扩张(14%)。二维超声心动图在30名受检者中有3人记录到典型的主动脉下突出。在对46例患者进行心电图检查时,4例出现房室传导阻滞,7例出现束支传导阻滞,10例患者传导系统受累。在并发淀粉样变性时,可以观察到淀粉样心脏浸润的典型表现。