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急性播散性脑脊髓炎中的钆环增强和占位效应。

Gadolinium ring enhancement and mass effect in acute disseminated encephalomyelitis.

作者信息

van der Meyden C H, de Villiers J F, Middlecote B D, Terblanchè J

机构信息

Department of Neurology, University of the Orange Free State, Bloemfontein, South Africa.

出版信息

Neuroradiology. 1994 Apr;36(3):221-3. doi: 10.1007/BF00588135.

DOI:10.1007/BF00588135
PMID:8041444
Abstract

A 9-year-old boy presented with a subacute history of optic neuritis followed by brainstem involvement, with fever and a lymphocytic pleocytosis in the cerebrospinal fluid. Gadolinium-enhancing ring lesions were demonstrated in the white matter of the cerebrum, brain-stem and cerebellum on day 17 of the illness, all appearing simultaneously as part of a monophasic illness. A parietal lesion exerted mass effect. Needling and biopsy yielded no evidence of a pyogenic lesion, tumour or tuberculosis and showed vasculitis. There was insufficient material for myelin staining. Dexamethasone therapy lead to rapid improvement of the radiological lesions: MRI and CT on day 34 of the illness showed complete clearing of the lesions except for residual abnormality at the biopsy site.

摘要

一名9岁男孩出现视神经炎亚急性病史,随后累及脑干,伴有发热及脑脊液淋巴细胞增多。病程第17天,大脑、脑干和小脑白质出现钆增强环形病变,均同时出现,为单相病程的一部分。顶叶病变产生占位效应。穿刺活检未发现化脓性病变、肿瘤或结核证据,显示为血管炎。髓鞘染色材料不足。地塞米松治疗使放射学病变迅速改善:病程第34天的MRI和CT显示病变完全消退,活检部位除外仍有残余异常。

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