Arceci R J
Harvard Medical School, Dana-Farber Cancer Institute, Boston, MA.
Br J Cancer Suppl. 1994 Sep;23:S58-60.
Although effective treatments are available for many children with LCH, there are many others for whom no definitive therapy yet exists. These patients include those with 1) multisystem disease and associated organ dysfunction, 2) chronic, relapsing disease, 3) new onset pituitary involvement associated with diabetes insipidus and 4) long-term complications such as pulmonary fibrosis, liver fibrosis or CNS involvement. This introductory paper discusses these clinical problem areas and then reviews several new therapeutic approaches including novel chemotherapeutic agents, immunosuppressive strategies, bone marrow transplantation and gene therapy.
虽然许多患有朗格汉斯细胞组织细胞增多症(LCH)的儿童可以获得有效的治疗,但仍有许多其他儿童尚无确切的治疗方法。这些患者包括:1)多系统疾病及相关器官功能障碍者;2)慢性复发性疾病患者;3)新发垂体受累伴尿崩症患者;4)患有肺纤维化、肝纤维化或中枢神经系统受累等长期并发症的患者。这篇引言性文章讨论了这些临床问题领域,然后回顾了几种新的治疗方法,包括新型化疗药物、免疫抑制策略、骨髓移植和基因治疗。