Languepin J, Daoud P, Desguerre I
Unité de réanimation médicale, hôpital Saint-Vincent-de-Paul, Paris, France.
Arch Pediatr. 1994 Jan;1(1):54-6.
Enterogenous cysts are benign embryogenic tumors that developed close to the central nervous system. They are rarely symptomatic in neonates. This report describes such a cyst in a young infant that was discovered because of the discomfort it produced.
A 16 day-old boy suffered from discomfort during bathing followed by deviation of the eyes. He was given diazepam rectally. At admission, he had generalized hypotonia and hyperreflexia. CSF examination showed 1.7 g/l protein. A prolonged apnea with cyanosis and bradycardia required his admission to the intensive care unit, where a spastic quadriparesis with bilateral phrenic nerve paralysis was found. EEG and brain ultrasonography were normal. MR imaging showed an intraspinal cyst, locating from C1 to C3, that was compressing the spinal cord. The cyst was rapidly excised and histological examination confirmed that it was an enterogenous cyst.
This cyst was not associated with vertebral abnormalities but did produce early symptoms. It was diagnosed by MR imaging.
肠源性囊肿是一种在中枢神经系统附近发育的良性胚胎性肿瘤。它们在新生儿中很少有症状。本报告描述了一名因产生不适而被发现的幼儿中的此类囊肿。
一名16天大的男孩在洗澡时感到不适,随后出现眼睛偏斜。给他直肠注射了地西泮。入院时,他有全身肌张力减退和反射亢进。脑脊液检查显示蛋白质含量为1.7g/l。一次伴有青紫和心动过缓的长时间呼吸暂停需要他入住重症监护病房,在那里发现了伴有双侧膈神经麻痹的痉挛性四肢瘫。脑电图和脑超声检查正常。磁共振成像显示一个位于C1至C3的脊髓内囊肿,压迫脊髓。囊肿被迅速切除,组织学检查证实为肠源性囊肿。
该囊肿与椎体异常无关,但确实产生了早期症状。它通过磁共振成像得以诊断。