Williams L L, Rooney C M, Conley M E, Brenner M K, Krance R A, Heslop H E
Department of Hematology/Oncology, St Jude Children's Research Hospital, Memphis, Tennessee.
Lancet. 1993 Sep 4;342(8871):587-8. doi: 10.1016/0140-6736(93)91413-g.
Duncan's syndrome (X-linked lymphoproliferative disorder) is a fatal immunodeficiency syndrome of unknown aetiology and without cure. We show that allogeneic bone marrow transplantation can correct the lethal immune deficits in a patient with this syndrome. We suggest that the primary abnormality in Duncan's syndrome is in bone-marrow derived cells.
邓肯综合征（X连锁淋巴增殖性疾病）是一种病因不明且无法治愈的致命免疫缺陷综合征。我们发现，异基因骨髓移植能够纠正患有该综合征患者的致命免疫缺陷。我们认为，邓肯综合征的原发性异常在于骨髓来源的细胞。
