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原发性卵巢类癌切除术后的进行性类癌性心脏病

Progressive carcinoid heart disease after resection of primary ovarian carcinoid.

作者信息

Wilkowske M A, Hartmann L C, Mullany C J, Behrenbeck T, Kvols L K

机构信息

Division of Medical Oncology, Mayo Clinic, Rochester, MN 55905.

出版信息

Cancer. 1994 Apr 1;73(7):1889-91. doi: 10.1002/1097-0142(19940401)73:7<1889::aid-cncr2820730719>3.0.co;2-3.

DOI:10.1002/1097-0142(19940401)73:7<1889::aid-cncr2820730719>3.0.co;2-3
PMID:8137216
Abstract

Primary ovarian carcinoid tumors are uncommon, and carcinoid heart disease is a rare complication. Although carcinoid syndrome and carcinoid heart disease typically occur in the setting of metastatic carcinoid tumor, particularly involving the liver, this is not necessarily the case in patients with primary ovarian carcinoid tumors. After surgical resection of an ovarian carcinoid tumor, the prognosis is excellent; however, carcinoid heart disease can continue to progress. The following is a case report of a patient who, despite having complete resection of a primary ovarian carcinoid tumor, went on to develop progressive, debilitating carcinoid heart disease. This is an important scenario to recognize, because proper management and surgical intervention in carcinoid heart disease can be lifesaving.

摘要

原发性卵巢类癌肿瘤并不常见,类癌性心脏病是一种罕见的并发症。虽然类癌综合征和类癌性心脏病通常发生在转移性类癌肿瘤的情况下,尤其是累及肝脏时,但原发性卵巢类癌肿瘤患者并非一定如此。卵巢类癌肿瘤手术切除后,预后良好;然而,类癌性心脏病可能会继续进展。以下是一例患者的病例报告,该患者尽管原发性卵巢类癌肿瘤已完全切除,但仍发展为进行性、使人衰弱的类癌性心脏病。这是一个需要认识到的重要情况,因为对类癌性心脏病进行适当的管理和手术干预可能会挽救生命。

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