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心尖肥厚型心肌病

Apical hypertrophic cardiomyopathy.

作者信息

Smolders W, Rademakers F, Conraads V, Snoeck J

机构信息

Department of Cardiology, University Hospital of Antwerp, Belgium.

出版信息

Acta Cardiol. 1993;48(4):369-83.

PMID:8212971
Abstract

Illustrated by a case report, which was rather suggestive of coronary ischemic heart disease, the principle characteristics of apical hypertrophic cardiomyopathy are outlined. Outside East Asia, it remains a very uncommon variant of hypertrophic cardiomyopathy. The electrocardiogram in basal conditions showed giant negative T-waves (-14 mm) in the precordial leads, while the ventriculogram in RAO projection revealed the typical, so called "ace of spades" configuration. Based on the present literature and the follow-up of these patients a review of apical hypertrophic cardiomyopathy is presented. One of the most important consequences of the identification of this variant seems to be the rather good prognosis when compared to other forms of hypertrophic cardiomyopathy.

摘要

通过一份颇具冠状动脉缺血性心脏病提示性的病例报告,概述了心尖肥厚型心肌病的主要特征。在东亚以外地区,它仍然是肥厚型心肌病中一种非常罕见的变异类型。基础状态下的心电图显示胸前导联出现巨大负向T波(-14毫米),而右前斜位心室造影显示出典型的所谓“黑桃A”形态。基于现有文献以及对这些患者的随访,对心尖肥厚型心肌病进行了综述。识别出这种变异类型最重要的后果之一似乎是,与其他形式的肥厚型心肌病相比,其预后相当良好。

相似文献

1
Apical hypertrophic cardiomyopathy.心尖肥厚型心肌病
Acta Cardiol. 1993;48(4):369-83.
2
[Regression of giant negative T waves in hypertrophic cardiomyopathy: cases simulating either dilated cardiomyopathy or severe coronary artery stenosis].肥厚型心肌病中巨大负向T波的消退:模拟扩张型心肌病或严重冠状动脉狭窄的病例
J Cardiol. 1988 Sep;18(3):875-85.
3
[Correlation between left ventricular wall thickness and the depth of negative T waves in apical hypertrophic cardiomyopathy].[肥厚型心肌病心尖部左心室壁厚度与T波倒置深度的相关性]
J Cardiogr. 1984 Aug;14(2):281-8.
4
Apical aneurysm in a patient with apical hypertrophic cardiomyopathy.一名患有心尖肥厚型心肌病患者的心尖部动脉瘤。
Conn Med. 2006 May;70(5):297-300.
5
Diagnosis of apical hypertrophic cardiomyopathy using magnetic resonance imaging.使用磁共振成像诊断心尖肥厚型心肌病。
Heart. 2000 Jan;83(1):E1. doi: 10.1136/heart.83.1.e1.
6
Apical hypertrophic cardiomyopathy mimicking acute coronary syndrome: a case report and review of the literature.酷似急性冠状动脉综合征的肥厚型心肌病:一例报告并文献复习
Angiology. 2008 Oct-Nov;59(5):629-31. doi: 10.1177/0003319707306447. Epub 2008 Apr 2.
7
[Do giant negative T waves represent apical hypertrophic cardiomyopathy? Left ventriculographic and cardiac biopsy studies].[巨大倒置T波代表心尖肥厚型心肌病吗?左心室造影及心脏活检研究]
J Cardiogr Suppl. 1985(6):35-51.
8
Call a Spade a Spade: Missed Diagnosis of Apical Hypertrophic Cardiomyopathy.直言不讳:误诊为心尖肥厚型心肌病。
Am J Med Sci. 2019 Oct;358(4):299-303. doi: 10.1016/j.amjms.2019.07.002. Epub 2019 Jul 13.
9
SPECT imaging of apical hypertrophic cardiomyopathy.
Clin Nucl Med. 2002 Nov;27(11):785-7. doi: 10.1097/00003072-200211000-00006.
10
[Apical hypertrophic cardiomyopathy: an element in the continuum of hypertrophic cardiomyopathies].[心尖肥厚型心肌病:肥厚型心肌病连续谱中的一个要素]
Presse Med. 1985 Sep 21;14(31):1645-8.

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