Leca-Chétochine F, Thibert M, Neveux J Y, Louville Y, Fiedmeyer A, Mathey J
Arch Mal Coeur Vaiss. 1976 Jun;69(6):639-44.
The series presented consists of 25 babies (18 of which were neonates), seen between 1972 and 1974. The anatomical and angiographic study revealed 5 anatomical types, according to whether the pulmonary orifice was patent or atretic, and according to the size of cavity of the right ventricle, which may be normal or reduced (perhaps almost totally). The diagnostic clinical features and findings on angiography are recalled. The operative procedure in all 25 cases was pulmonary valvotomy carried out with a brief normothermic period of cirulatory arrest. The technique is described briefly. The results, which vary widely with the anatomical type, were as follows: out of the 25 operated cases there were 12 deaths during or immediately after surgery. The figures are none-the-less encouraging, given the grave natural history of this condition in the baby. The best results were seen in cases in which there was a right ventricular cavity of normal or at least acceptable size. The maximum postoperative follow-up period was 3 years. Most of these children have a persistant pulmonary stenosis and hypertrophic right ventricle, and require a second operation in early infancy.
该系列病例包括1972年至1974年间诊治的25例婴儿(其中18例为新生儿)。解剖学和血管造影研究根据肺动脉口是开放还是闭锁,以及右心室腔的大小(可能正常或缩小,甚至几乎完全缩小),揭示了5种解剖类型。回顾了诊断性临床特征和血管造影结果。所有25例病例的手术方法均为肺动脉瓣切开术,手术过程中进行了短暂的常温循环阻断。简要描述了该技术。结果因解剖类型而异,如下所示:25例手术病例中有12例在手术期间或术后立即死亡。不过,鉴于婴儿期这种疾病的严重自然病程,这些数字仍然令人鼓舞。右心室腔大小正常或至少可接受的病例效果最佳。术后最长随访期为3年。这些儿童大多数存在持续性肺动脉狭窄和肥厚性右心室,需要在婴儿早期进行二次手术。