Gerritsen R T, Spoelstra P, Breeuwsma N G
Department of Internal Medicine, Medical Centre, Leeuwarden, Netherlands.
Neth J Med. 1993 Aug;43(1-2):22-5.
Familial adenomatous polyposis (FAP) is characterized by the development of adenomas throughout the entire gastrointestinal tract. We describe a brother and sister with FAP who developed adenocarcinoma around the papilla of Vater. Incidence, premalignancy, treatment and the need for prophylactic endoscopy are discussed.