Ohtsuka G, Tsuchiya K, Noji S, Suzuki S, Sasaki H, Iida Y
Department of Cardiovascular Surgery, Yamanashi Prefectural Central Hospital.
Nihon Kyobu Geka Gakkai Zasshi. 1993 Nov;41(11):2250-5.
A 54-year-old man suffered from tetralogy of Fallot associated with aortic valve regurgitation, coronary artery-pulmonary artery fistula and absent pulmonary valve underwent intracardiac repair. The operation was completed with ligation of the fistula, aortic valve replacement using a SJM 27 A, patch closure of ventricular septal defect (perimembranous outlet type) and right ventricular outflow reconstruction using a large transannular monocusped-patch, 4 cm x 6 cm in size. Postoperative course was uneventful and he is doing well now. There was no previous reports about TOF associated with AR, the absent pulmonary valve and the coronary anomaly in the adults in the literature.
一名54岁男性患有法洛四联症，合并主动脉瓣反流、冠状动脉-肺动脉瘘及肺动脉瓣缺如，接受了心内修复手术。手术通过结扎瘘管、使用SJM 27 A型人工瓣膜置换主动脉瓣、补片修补室间隔缺损（膜周流出道型）以及使用一块大小为4厘米×6厘米的大型跨环单瓣补片进行右心室流出道重建得以完成。术后过程顺利，他目前情况良好。文献中此前尚无关于成人法洛四联症合并主动脉瓣反流、肺动脉瓣缺如及冠状动脉异常的报道。
