Serino W, Argento G, Fiorilli R, Di Benedetto G, Velitti F
Divisione di Cardiologia Emodinamica, Ospedale S Carlo, Potenza.
Cardiologia. 1993 Aug;38(8):531-4.
We illustrate a case of so-called right pulmonary artery agenesis, discovered in a 3-month-old baby. This kind of malformation is rarely reported in neonatal age being most often discovered in the adulthood. The patient presented with cardiac failure, cyanosis and radiological features of cardiomegaly and left side pulmonary venous congestion. The diagnosis was strongly suspected by two-dimensional echocardiography and confirmed at cardiac catheterization. The patient was successfully operated upon with connection of main pulmonary artery to hilar right pulmonary artery. To the best of our knowledge, this is the first reported case of diagnosis and effective surgical therapy of right pulmonary artery agenesis in neonatal age.
我们阐述了一例在一名3个月大婴儿中发现的所谓右肺动脉发育不全病例。这种畸形在新生儿期很少有报道，大多是在成年期发现。该患者表现为心力衰竭、发绀以及心脏扩大和左侧肺静脉淤血的放射学特征。二维超声心动图强烈怀疑该诊断，并在心脏导管检查时得以证实。通过将主肺动脉与右侧肺门肺动脉相连，该患者成功接受了手术。据我们所知，这是新生儿期右肺动脉发育不全诊断及有效手术治疗的首例报道病例。
