Espinosa R E, Edwards W D, Rosenow E C, Schaff H V
Division of Cardiovascular Diseases and Internal Medicine, Mayo Clinic Rochester, Minnesota 55905.
Mayo Clin Proc. 1993 Aug;68(8):778-82. doi: 10.1016/s0025-6196(12)60636-3.
A 37-year-old man with progressive exertional dyspnea had pulmonary hypertension associated with pulmonary arterial and venous obstruction. An autopsy revealed that the cause of death was idiopathic pulmonary hilar fibrosis, a variant of mediastinal fibrosis. Pulmonary hilar fibrosis can mimic thromboembolic pulmonary hypertension, pulmonary veno-occlusive disease, and pulmonary venous hypertension.
一名37岁男性，进行性劳力性呼吸困难，患有与肺动脉和静脉阻塞相关的肺动脉高压。尸检显示，死亡原因是特发性肺门纤维化，这是纵隔纤维化的一种变体。肺门纤维化可模仿血栓栓塞性肺动脉高压、肺静脉闭塞性疾病和肺静脉高压。
