Vogt-Moykopf I, Rau B, Branscheid D
Thoraxklinik, Heidelberg-Rohr-Bach, Germany.
Ann Radiol (Paris). 1993;36(2):145-60.
In the course of a survey conducted in 59 hospitals performing thoracic surgery, 14 hospitals supplied data that could be used for the study. Out of 1347 anomalies diagnosed 1343 were surgically treated, with a 30-day mortality rate of 0.3% (5 patients). In a retrospective study over a period of 10 years (1978-1988) we identified 198 anomalies out of a total of 6350 thoracotomies; so our percentage grading of pulmonary anomalies is supported by the data of the above-mentioned survey according to which cystic pulmonary malformations such as inhibition malformations, excess malformation and lobar emphysema represent a majority with 72.2% (survey 83%). Congenital anomalies of lung formation occurred in 23% of the patients of the survey and in 15% of our own patients. Therapy consisted of parenchyma-saving surgery, i.e. enucleation (n = 87), segmental resection (n = 65) and lobectomy (n = 63) with bronchoplastic reconstruction; there was no 30-day mortality. Adenomatoid-cystic malformation, lymphangiectasis, congenital lobar emphysema and stenosis of the tracheobronchial tree are often an indication for immediate surgical treatment in neonates. Solitary cysts, bronchiectasis, sequestration of the lung, an AV-fistula present with symptoms mostly between the ages of 20-40 and therefore were surgically treated secondarily.
在对59家开展胸外科手术的医院进行的一项调查过程中，14家医院提供了可用于该研究的数据。在诊断出的1347例异常病例中，1343例接受了手术治疗，30天死亡率为0.3%（5例患者）。在一项为期10年（1978 - 1988年）的回顾性研究中，我们在总共6350例开胸手术中识别出198例异常；因此，我们对肺部异常的百分比分级得到了上述调查数据的支持，根据该调查，诸如抑制性畸形、过度畸形和大叶性肺气肿等囊性肺畸形占多数，为72.2%（调查中为83%）。肺部形成的先天性异常在调查患者中的发生率为23%，在我们自己的患者中为15%。治疗包括保留实质的手术，即摘除术（n = 87）、节段性切除术（n = 65）和肺叶切除术（n = 63）并进行支气管成形重建；无30天死亡率。腺样囊性畸形、淋巴管扩张、先天性大叶性肺气肿和气管支气管树狭窄通常是新生儿立即进行手术治疗的指征。孤立性囊肿、支气管扩张、肺隔离症、动静脉瘘大多在20至40岁之间出现症状，因此接受二期手术治疗。
