Surfactant apoprotein B deficiency.
作者信息
Chetcuti P A, Ball R J
机构信息
Department of Paediatrics, Leeds General Infirmary.
出版信息
Arch Dis Child Fetal Neonatal Ed. 1995 Nov;73(3):F125-7. doi: 10.1136/fn.73.3.f125.
Abstract
摘要
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Cell-specific posttranslational processing of the surfactant-associated protein SP-B.表面活性物质相关蛋白SP-B的细胞特异性翻译后加工
Am J Physiol. 1993 Mar;264(3 Pt 1):L290-9. doi: 10.1152/ajplung.1993.264.3.L290.
2
Differential glucocorticoid regulation of the pulmonary hydrophobic surfactant proteins SP-B and SP-C.糖皮质激素对肺疏水表面活性蛋白SP-B和SP-C的差异调节
Am J Respir Cell Mol Biol. 1993 Feb;8(2):222-8. doi: 10.1165/ajrcmb/8.2.222.
3
Brief report: deficiency of pulmonary surfactant protein B in congenital alveolar proteinosis.简短报告：先天性肺泡蛋白沉积症中肺表面活性物质蛋白B缺乏
N Engl J Med. 1993 Feb 11;328(6):406-10. doi: 10.1056/NEJM199302113280606.
4
A function of lung surfactant protein SP-B.肺表面活性物质蛋白SP-B的一种功能。
Science. 1993 Jul 23;261(5120):453-6. doi: 10.1126/science.8332910.
5
Surfactant protein B deficiency: radiographic manifestations.表面活性物质蛋白B缺乏症：影像学表现。
Pediatr Radiol. 1993;23(5):373-5. doi: 10.1007/BF02011963.
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A mutation in the surfactant protein B gene responsible for fatal neonatal respiratory disease in multiple kindreds.一种在多个家族中导致致命性新生儿呼吸系统疾病的表面活性蛋白B基因突变。
J Clin Invest. 1994 Apr;93(4):1860-3. doi: 10.1172/JCI117173.
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Adenoviral-mediated gene transfer of human surfactant protein B to respiratory epithelial cells.腺病毒介导的人表面活性蛋白B基因向呼吸道上皮细胞的转移。
Am J Respir Cell Mol Biol. 1994 Sep;11(3):329-36. doi: 10.1165/ajrcmb.11.3.8086169.
8
Surfactant protein B deficiency: antenatal diagnosis and prospective treatment with surfactant replacement.
J Pediatr. 1994 Sep;125(3):356-61. doi: 10.1016/s0022-3476(05)83276-7.
9
Molecular and phenotypic variability in the congenital alveolar proteinosis syndrome associated with inherited surfactant protein B deficiency.与遗传性表面活性物质蛋白B缺乏相关的先天性肺泡蛋白沉积症综合征的分子和表型变异性。
J Pediatr. 1994 Jul;125(1):43-50. doi: 10.1016/s0022-3476(94)70119-9.
10
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Biol Neonate. 1995;67 Suppl 1:2-17. doi: 10.1159/000244202.
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