Noronha C F, Alves Duro L A
Instituto de Neurologia Deolindo Couto (INDC), Universidade Federal do Rio de Janeiro (UFRJ), Brasil.
Arq Neuropsiquiatr. 1995 Sep;53(3-A):424-31.
Orofacial examination was applied in 39 patients with myotonic dystrophy. We made an original table with a scale of punctuation. The group showed a deficit of 43.70%. The female group was 6.16% better than male's. The maternal inherited cases were 3.63% better than the paternal ones. When we separated the groups by decades, there was a tendency to an increasingly better performance as the age of the beggining of symptoms was later. The performance was 10.68% better in the group of patients with 1 to 10 years than in the group with 11 to 20 years of disease. We concluded that the phonoaudiological affection in myotonic dystrophy was less intense in patients with later onset of symptoms and less than 10 years of disease.
对39例强直性肌营养不良患者进行了口面部检查。我们制作了一个带有评分量表的原始表格。该组显示出43.70%的缺陷。女性组比男性组好6.16%。母系遗传病例比父系遗传病例好3.63%。当我们按十年划分组时，随着症状开始年龄越晚，表现有越来越好的趋势。发病1至10年的患者组比发病11至20年的患者组表现好10.68%。我们得出结论，强直性肌营养不良患者中，症状出现较晚且患病时间少于10年的患者，其听觉语音障碍程度较轻。
