Molina C, Alvarez Sabín J, Bosch J, Codina Puiggrós A
Servicio de Neurologia, Hospital Universitari Vall d'Hebron, Barcelona.
Rev Neurol. 1995 Nov-Dec;23(124):1242-5.
Moya-Moya disease is a chronic infrequent vasculopathy. Occasionally such abnormalities are found in association with one of many conditions, in these cases the angiographic abnormality should be termed Moya-Moya syndrome rather than Moya-Moya disease. Although in children the usual manifestations are ischemic events and seizures. This clinical presentation is infrequent in adults. We present a 42-years-old man with a 1-month history of recurrent right sided partial somatosensorial seizures, later he presented a left parietal infarction, the angiographic findings were compatible with moyamoya syndrome.
烟雾病是一种慢性罕见的血管病变。偶尔会在许多病症之一的情况下发现此类异常，在这些病例中，血管造影异常应称为烟雾综合征而非烟雾病。虽然在儿童中常见表现为缺血性事件和癫痫发作，但这种临床表现在成人中并不常见。我们报告一名42岁男性，有1个月复发性右侧部分躯体感觉性癫痫发作史，后来出现左侧顶叶梗死，血管造影结果符合烟雾综合征。
