Mattle H P, Maurer D, Sturzenegger M, Ozdoba C, Baumgartner R W, Schroth G
Department of Neurology, University of Bern, Inselspital, Switzerland.
J Neurol. 1995 Oct;242(10):689-94. doi: 10.1007/BF00866921.
From 1980 to 1992 we followed 12 patients with cardiac myxomas for an average of 4.4 years (8 months-11 years). Presenting symptoms were neurological in four patients (hemiparesis, aphasia, visual field deficits, progressive dementia or vertigo), progressive dyspnoea in six, pulmonary embolism in one, and peripheral arterial or renal emboli in three. The diagnosis was suspected clinically in 11 patients. It was confirmed by echocardiography in ten and by thoracic CT in one. All these patients had cardiac surgery. One diagnosis was made at autopsy; the patient died unexpectedly during surgery for emboli to the leg arteries. At follow-up, two additional patients had died, one from myocardial infarction and one from rhabdomyosarcoma. Only one of the nine surviving patients had recurrent symptoms after cardiac surgery. His dementia continued to progress. The patients without new symptoms after cardiac surgery had normal MRI of the brain or residual ischaemic lesions. MRI of the patient with progressive dementia showed multiple cerebral lesions with a bright centre and a dark rim on T1- and T2-weighted spin-echo images. On CT there were many calcified lesions. CT, MR angiography and contrast angiography revealed multiple fusiform aneurysms. The rare occurrence of progressive neurological symptoms after myxoma resection with multiple cerebral lesions and aneurysms should suggest myxoma metastases to the brain.
1980年至1992年期间,我们对12例心脏黏液瘤患者进行了平均4.4年(8个月至11年)的随访。4例患者的首发症状为神经系统症状(偏瘫、失语、视野缺损、进行性痴呆或眩晕),6例为进行性呼吸困难,1例为肺栓塞,3例为外周动脉或肾栓塞。11例患者临床怀疑有诊断。10例经超声心动图确诊,1例经胸部CT确诊。所有这些患者均接受了心脏手术。1例诊断在尸检时做出;该患者在腿部动脉栓塞手术中意外死亡。随访期间,又有2例患者死亡,1例死于心肌梗死,1例死于横纹肌肉瘤。9例存活患者中只有1例在心脏手术后出现复发症状。他的痴呆症继续进展。心脏手术后无新症状的患者脑部MRI正常或有残留缺血性病变。进行性痴呆患者的MRI在T1加权和T2加权自旋回波图像上显示多个脑病变,中心明亮,边缘黑暗。CT上有许多钙化病变。CT、磁共振血管造影和对比血管造影显示多个梭形动脉瘤。黏液瘤切除术后出现进行性神经症状并伴有多个脑病变和动脉瘤的情况罕见,应提示黏液瘤转移至脑部。