Zaloudek C, Miller T R, Stern J L
Department of Pathology, University of California, San Francisco 94143, USA.
Int J Gynecol Pathol. 1995 Jul;14(3):260-5. doi: 10.1097/00004347-199507000-00011.
Desmoplastic small cell tumor (DSCT) is a recently described intraabdominal neoplasm of uncertain histogenesis that occurs predominantly in boys and young men. We report a case in a young woman that presented clinically as bilateral ovarian tumors with extensive pelvic and abdominal dissemination. The patient had cytoreductive surgery followed by combination chemotherapy. She had a complete clinical remission, but tumor recurrence was detected 1 year after diagnosis and the patient died of her disease 18 months after presentation. DSCT has a distinctive histologic appearance and a unique immunophenotype. It can present as an ovarian neoplasm and must be considered in the differential diagnosis of small cell tumors of the ovary.
促结缔组织增生性小圆细胞肿瘤（DSCT）是一种最近才被描述的腹腔内肿瘤，其组织发生尚不明确，主要发生于男孩和青年男性。我们报告一例年轻女性病例，临床表现为双侧卵巢肿瘤并伴有广泛的盆腔和腹腔播散。该患者接受了肿瘤细胞减灭术，随后进行联合化疗。她获得了完全的临床缓解，但在诊断后1年检测到肿瘤复发，患者在就诊18个月后死于该疾病。DSCT具有独特的组织学表现和独特的免疫表型。它可表现为卵巢肿瘤，在卵巢小细胞肿瘤的鉴别诊断中必须予以考虑。
