Tanaka M, Suda M, Ishikawa Y, Fujitake J, Fujii H, Tatsuoka Y
Department of Medicine and Clinical Science, Kyoto University Graduate School of Medicine, Japan.
Neurology. 1996 Feb;46(2):554-6. doi: 10.1212/wnl.46.2.554.
We describe a patient with idiopathic hypertrophic cranial pachymeningitis (IHCP) associated with hydrocephalus and myocarditis in whom steroids caused remission of the hypertrophic dura and enlarged ventricles. Myocarditis induced complete atrioventricular block that responded to steroids initially but later required permanent pacemaker implantation. Serum ANA and anti-dsDNA antibody were positive. Our case suggests that IHCP and myocarditis may share a common autoimmune etiology.
我们描述了一名患有特发性肥厚性硬脑膜炎（IHCP）并伴有脑积水和心肌炎的患者，在该患者中，类固醇使肥厚的硬脑膜和扩大的脑室病情缓解。心肌炎导致完全性房室传导阻滞，最初对类固醇有反应，但后来需要植入永久性起搏器。血清抗核抗体（ANA）和抗双链DNA抗体呈阳性。我们的病例提示，IHCP和心肌炎可能有共同的自身免疫病因。
