Kelemen A, Bozić K, Ivetić V, Filipović D
Institut za neurologiju, psihijatriju i mentalno zdravlje Zavod za fiziologiju, Medicinski fakultet, Novi Sad.
Med Pregl. 1995;48(9-10):343-6.
Phacomatoses are hereditary disease caused by germinative matrix disorder. Apart from known proliferative and tumor processes on peripheral nerves and their roots which make up a familiar picture of this disease to all neurologist, other tissue and organ malformations of octo and mesodermal origin may occur. This is a case report of a girl with neurofibromatosis type I after Riccardi with occlusive hydrocephalus complication. We pointed to a great number of neurofibromatosis complications, their prompt detection and treatment.
错构瘤病是由生发基质紊乱引起的遗传性疾病。除了外周神经及其神经根上已知的增殖性和肿瘤性病变(这对所有神经科医生来说都是这种疾病的常见表现)之外,还可能出现起源于外胚层和中胚层的其他组织和器官畸形。这是一例患有I型神经纤维瘤病(按照里卡尔迪分型)并伴有梗阻性脑积水并发症的女孩的病例报告。我们指出了大量神经纤维瘤病的并发症、它们的早期发现及治疗。