Mohr P D, Strang F A, Sambrook M A, Boddie H G
Q J Med. 1977 Jan;46(181):85-96.
This paper reports 40 patients with primary cerebellar ectopia investigated in the University of Manchester departments of neurology and neurosurgery over the five years, 1968-1973. A review of the clinical and surgical findings showed that (a) pain of varying type was the most common symptom, (b) four main clinical groups could be recognized--syringomyelia, paraparesis, cerebellar syndrome and 'raised pressure' syndrome and (c) surgical decompression of the posterior fossa and upper cervical spine resulted in improvement in over 70 per cent of patients with a small incidence of post-operative complications. It should be emphasised that primary cerebellar ectopia is not uncommon and is an important syndrome in its own right. It is often not accompanied by syringomyelia and in these patients the diagnosis can be difficult without supine myelography.
本文报道了1968年至1973年这五年间在曼彻斯特大学神经科和神经外科接受检查的40例原发性小脑异位患者。对临床和手术结果的回顾显示：（a）不同类型的疼痛是最常见的症状；（b）可识别出四个主要临床组——脊髓空洞症、轻截瘫、小脑综合征和“颅内压升高”综合征；（c）后颅窝和上颈椎的手术减压使70%以上的患者病情得到改善，术后并发症发生率较低。应当强调的是，原发性小脑异位并不罕见，其本身就是一种重要的综合征。它常常不伴有脊髓空洞症，对于这些患者，如果不进行仰卧位脊髓造影，诊断可能会很困难。
