Okano T, Ioka J, Tanabe S, Nakane Y, Nishiyama K
Department of Surgery, Ohmihachiman City Hospital, Shiga, Japan.
Nihon Kyobu Geka Gakkai Zasshi. 1996 Jan;44(1):69-73.
We report a pulmonary blastoma lacking sarcomatous features in 33-year-old woman. Abnormal shadow was detected in the right upper field in a routine chest X-ray film. The preoperative imaging films showed a 4 x 4 cm, well-circumscribed solid tumor in S3 of the right lung. The preoperative clinical diagnosis of primary lung cancer was considered. The operative findings showed that an elastic hard tumor, 5 cm in diameter, was localized in S3 of the right lung and partially contacted the middle lobe. Right upper and middle lobe resection was performed with lymph node dissection. The postoperative diagnosis was pulmonary blastoma, well differentiated fetal lung (= WDFA). It is considered that the degree of the malignancy of WDFA is lower and the prognosis of WDFA is better than conventional pulmonary blastoma (= biphasic blastoma). There are not available treatments except for surgical resection. It is suggested that it necessary to collect as many cases as possible, to make definite classifications and to examine the clinical course and prognosis of pulmonary blastoma.
我们报告了一名33岁女性患有的无肉瘤特征的肺母细胞瘤。在常规胸部X光片中，右上肺野发现异常阴影。术前影像学检查显示右肺S3区有一个4×4厘米、边界清晰的实性肿瘤。术前临床诊断考虑为原发性肺癌。手术所见显示，一个直径5厘米的弹性硬肿瘤位于右肺S3区，部分与中叶相连。行右上叶和中叶切除并清扫淋巴结。术后诊断为肺母细胞瘤，高分化胎儿型肺母细胞瘤（=WDFA）。据认为，WDFA的恶性程度低于传统肺母细胞瘤（=双相性母细胞瘤），其预后也更好。除手术切除外，尚无其他可用治疗方法。建议尽可能多地收集病例，进行明确分类，并研究肺母细胞瘤的临床病程和预后。
