多灶性贝斯特卵黄样营养不良

Multifocal Best's vitelliform dystrophy.

作者信息

Miller S A

出版信息

Arch Ophthalmol. 1977 Jun;95(6):984-90. doi: 10.1001/archopht.1977.04450060070004.

DOI:10.1001/archopht.1977.04450060070004

Abstract

Three members of a family had multifocal, macular and extramacular--Best's vitelliform dystrophy. The lesion in one patient was observed over a ten-year period. A striking symmetry of locale and evolution of these lesions is noted between the eyes of a patient as well as among the three members of the family. The pseudohypopyon of the vitelliform cyst and the vitelliform deposits showed fluorescence before fluorescein injection. A hypofluorescent halo surrounded most lesions.

摘要

一个家庭的三名成员患有多灶性、黄斑及黄斑外——贝斯特卵黄样营养不良。对一名患者的病变进行了为期十年的观察。在一名患者的双眼之间以及该家庭的三名成员之间，这些病变在位置和发展上呈现出显著的对称性。卵黄样囊肿的假性前房积脓和卵黄样沉积物在注射荧光素前显示出荧光。大多数病变周围有低荧光晕。