Banai J, Kendrey G, Virágh S, Fenyvesi A, Jánosi J
Haynal Imre Egészségtudományi Egyetem, Budapest, I. Belgyógyászati Klinika.
Orv Hetil. 1996 Feb 25;137(8):415-9.
A family (three siblings) of Wilson's-disease is described. The authors review the pathogenesis, diagnostics, pathology and treatment of Wilson's-disease. The diagnostic difficulties are emphasised. The variety of liver lesions are demonstrated in the different grades of the disease. The importance of the early diagnosis is stressed.
本文描述了一个威尔逊氏病家族(三兄弟姐妹)。作者回顾了威尔逊氏病的发病机制、诊断、病理及治疗。强调了诊断上的困难。展示了该病不同阶段各种肝脏病变情况。强调了早期诊断的重要性。