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发热性溃疡性坏死性穆查-哈伯曼病:一例报告并文献复习

Febrile ulceronecrotic Mucha-Habermann disease: a case report and review of the literature.

作者信息

Suárez J, López B, Villalba R, Perera A

机构信息

Section of Dermatology, Hospital La Candelaria, Santa Cruz de Tenerife, Spain.

出版信息

Dermatology. 1996;192(3):277-9. doi: 10.1159/000246385.

DOI:10.1159/000246385
PMID:8726649
Abstract

A 32-year-old male with febrile ulceronecrotic Mucha-Habermann disease (FUMHD) responsive to methotrexate is reported. This is a severe variant of pityriasis lichenoides et varioliformis acuta characterized by the acute onset of a widespread ulceronecrotic cutaneous eruption together with high fever and systemic involvement. To our knowledge, only 13 patients with FUMHD have been reported to date.

摘要

报告了一名32岁男性,患有对甲氨蝶呤有反应的发热性溃疡性坏死性穆查-哈伯曼病(FUMHD)。这是急性痘疮样苔藓样糠疹的一种严重变体,其特征为广泛的溃疡性坏死性皮肤疹急性发作,伴有高热和全身受累。据我们所知,迄今为止仅报告了13例FUMHD患者。

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引用本文的文献

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Dermatol Reports. 2022 Nov 21;14(4):9492. doi: 10.4081/dr.2022.9492.
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Febrile ulceronecrotic Mucha-Habermann disease.发热性溃疡性坏死性穆查-哈伯曼病
BMJ Case Rep. 2013 Oct 14;2013:bcr2013009739. doi: 10.1136/bcr-2013-009739.
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Conjunctival Inflammatory Nodule in a Patient with Pityriasis Lichenoides et Varioliformis Acuta.
急性痘疮样苔藓样糠疹患者的结膜炎性结节
Case Rep Dermatol. 2010 Jul 12;2(2):125-129. doi: 10.1159/000315443.