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Glycerol trioleate/glycerol trierucate therapy in X-linked adrenoleukodystrophy: saturated and unsaturated fatty acids in blood cells. Implications for the follow-up.

作者信息

Ruiz M, Pampols T, Girós M

机构信息

Institut de Bioquímica Clínica, Avinguda Flor de maig s/n, Barcelona, Spain.

出版信息

J Inherit Metab Dis. 1996;19(2):188-92. doi: 10.1007/BF01799426.

DOI:10.1007/BF01799426
PMID:8739962
Abstract
摘要

相似文献

1
Glycerol trioleate/glycerol trierucate therapy in X-linked adrenoleukodystrophy: saturated and unsaturated fatty acids in blood cells. Implications for the follow-up.甘油三油酸酯/甘油三芥酸酯疗法治疗X连锁肾上腺脑白质营养不良:血细胞中的饱和脂肪酸和不饱和脂肪酸。对随访的意义。
J Inherit Metab Dis. 1996;19(2):188-92. doi: 10.1007/BF01799426.
2
Very long chain fatty acids in X-linked adrenoleukodystrophy brain after treatment with Lorenzo's oil.使用洛伦佐油治疗后X连锁肾上腺脑白质营养不良症患者大脑中的极长链脂肪酸
Ann Neurol. 1994 Nov;36(5):741-6. doi: 10.1002/ana.410360509.
3
Evaluation of the preventive effect of glyceryl trioleate-trierucate ("Lorenzo's oil") therapy in X-linked adrenoleukodystrophy: results of two concurrent trials.甘油三油酸酯-三芥酸酯(“洛伦佐油”)疗法对X连锁肾上腺脑白质营养不良预防效果的评估:两项同期试验的结果
Adv Exp Med Biol. 2003;544:369-87. doi: 10.1007/978-1-4419-9072-3_47.
4
Treatment of X-linked adrenoleukodystrophy with Lorenzo's oil.用洛伦佐油治疗X连锁肾上腺脑白质营养不良。
J Neurol Neurosurg Psychiatry. 1999 Sep;67(3):279-80. doi: 10.1136/jnnp.67.3.279.
5
Visual evoked potentials in adrenoleukodystrophy: a trial with glycerol trioleate and Lorenzo oil.肾上腺脑白质营养不良中的视觉诱发电位:甘油三油酸酯和洛伦佐油试验
Ann Neurol. 1993 Aug;34(2):169-74. doi: 10.1002/ana.410340212.
6
Follow-up of 89 asymptomatic patients with adrenoleukodystrophy treated with Lorenzo's oil.对89例接受洛伦佐油治疗的无症状肾上腺脑白质营养不良患者的随访。
Arch Neurol. 2005 Jul;62(7):1073-80. doi: 10.1001/archneur.62.7.1073.
7
Lorenzo's oil: advances in the treatment of neurometabolic disorders.洛伦佐之油:神经代谢紊乱治疗的进展
Arch Neurol. 2005 Jul;62(7):1045-6. doi: 10.1001/archneur.62.7.1045.
8
Enhanced lymphocyte proliferation in patients with adrenoleukodystrophy treated with erucic acid (22:1)-rich triglycerides.
J Inherit Metab Dis. 2000 Mar;23(2):113-9. doi: 10.1023/a:1005657530372.
9
Komrower Lecture. Adrenoleukodystrophy: natural history, treatment and outcome.科姆罗尔讲座。肾上腺脑白质营养不良:自然病史、治疗与预后
J Inherit Metab Dis. 1995;18(4):435-47. doi: 10.1007/BF00710055.
10
[Diet therapy with erucic acid in patients with X-linked adrenoleukodystrophy].[二十二碳单烯酸饮食疗法治疗X连锁肾上腺脑白质营养不良患者]
Minerva Pediatr. 1991 Mar;43(3):127-31.

引用本文的文献

1
Hexacosanoic and docosanoic acids plasma levels in patients with cerebral childhood and asymptomatic X-linked adrenoleukodystrophy: Lorenzo's oil effect.患有儿童期脑型和无症状X连锁肾上腺脑白质营养不良患者的血浆二十六烷酸和二十二烷酸水平:洛伦佐油的作用。
Metab Brain Dis. 2008 Mar;23(1):43-9. doi: 10.1007/s11011-007-9079-9. Epub 2007 Nov 17.

本文引用的文献

1
Profiles of very-long-chain fatty acids in plasma, fibroblasts, and blood cells in Zellweger syndrome, X-linked adrenoleukodystrophy, and rhizomelic chondrodysplasia punctata.泽尔韦格综合征、X连锁肾上腺脑白质营养不良和点状软骨发育不良中血浆、成纤维细胞和血细胞中极长链脂肪酸的谱。
Clin Chem. 1993 Aug;39(8):1632-7.
2
A two-year trial of oleic and erucic acids ("Lorenzo's oil") as treatment for adrenomyeloneuropathy.一项使用油酸和芥酸(“洛伦佐之油”)治疗肾上腺脑白质营养不良的两年试验。
N Engl J Med. 1993 Sep 9;329(11):745-52. doi: 10.1056/NEJM199309093291101.
3
Covalent modification of proteins by arachidonate and eicosapentaenoate in platelets.
血小板中花生四烯酸和二十碳五烯酸对蛋白质的共价修饰。
J Biol Chem. 1993 Aug 25;268(24):18243-8.
4
Thrombocytopenia induced by erucic acid therapy in patients with X-linked adrenoleukodystrophy.X连锁肾上腺脑白质营养不良患者中芥酸治疗引起的血小板减少症。
Clin Investig. 1993 Oct;71(10):802-5. doi: 10.1007/BF00190322.
5
Glyceroltrioleate/glyceroltrierucate therapy in 16 patients with X-chromosomal adrenoleukodystrophy/adrenomyeloneuropathy: effect on clinical, biochemical and neurophysiological parameters.
Eur J Pediatr. 1995 Jan;154(1):64-70. doi: 10.1007/BF01972976.
6
Dietary treatment of adrenoleukodystrophy.
Neurology. 1986 Jan;36(1):104-6. doi: 10.1212/wnl.36.1.104.
7
Adrenoleukodystrophy: dietary oleic acid lowers hexacosanoate levels.肾上腺脑白质营养不良:膳食油酸可降低二十六烷酸水平。
Ann Neurol. 1987 Mar;21(3):232-9. doi: 10.1002/ana.410210304.
8
Dietary erucic acid therapy for X-linked adrenoleukodystrophy.用于X连锁肾上腺脑白质营养不良的膳食芥酸疗法。
Neurology. 1989 Nov;39(11):1415-22. doi: 10.1212/wnl.39.11.1415.
9
A comparison of erythrocytes, lymphocytes and blood plasma as samples in fatty acid analysis for the diagnosis of adrenoleukodystrophy.
J Neurol Sci. 1989 Dec;94(1-3):193-200. doi: 10.1016/0022-510x(89)90229-3.
10
Physiological significance of fatty acid elongation system in adrenoleukodystrophy.肾上腺脑白质营养不良中脂肪酸延长系统的生理意义。
J Neurol Sci. 1991 Jun;103(2):188-94. doi: 10.1016/0022-510x(91)90163-2.