Halliday J W, Searle J
Queensland Institute of Medical Research, Bancroft Centre, Brisbane, Queensland, Australia.
Biometals. 1996 Apr;9(2):205-9. doi: 10.1007/BF00144626.
Iron deposition occurs in parenchymal cells of the liver in two major defects in human subjects (i) in primary iron overload (genetic haemochromatosis) and (ii) secondary to anaemias in which erythropolesis is increased (thalassaemia). Transfusional iron overload results in excessive storage primarily in cells of the reticule endothelial system. The storage patterns in these situations are quite characteristic. Excessive iron storage, particularly in parenchymal cells eventually results in fibrosis and cirrhosis. There is no animal model or iron overload which completely mimics genetics haemochromatosis but dietary iron loading with carbonyl iron or ferrocene does produce excessive parenchymal iron stores in the rat. Such models have been used to study iron toxicity and the action of iron chelators in the effective removal of excessive iron stores.
在人类受试者中,铁沉积发生在肝脏实质细胞中,主要存在于两种主要缺陷中:(i)原发性铁过载(遗传性血色素沉着症),以及(ii)继发于红细胞生成增加的贫血(地中海贫血)。输血性铁过载主要导致铁在网状内皮系统细胞中过度储存。这些情况下的储存模式非常具有特征性。过量的铁储存,特别是在实质细胞中,最终会导致纤维化和肝硬化。目前尚无完全模拟遗传性血色素沉着症的动物铁过载模型,但用羰基铁或二茂铁进行饮食性铁负荷确实会在大鼠体内产生过量的实质铁储存。此类模型已被用于研究铁毒性以及铁螯合剂在有效清除过量铁储存方面的作用。