Fisher C A, LeBoit P E, Frieden I J
Dermatology Department, National Naval Medical Center, Bethesda, Maryland, USA.
Pediatr Dermatol. 1995 Dec;12(4):318-22. doi: 10.1111/j.1525-1470.1995.tb00192.x.
The classic appearance of porokeratosis is characterized by a hyperkeratotic annular rim that expands peripherally, leaving an atrophic center. Linear porokeratosis is a variant with collections of such lesions arranged in a linear fashion, usually corresponding to a dermatome or Blaschko's lines. Ulcerations have rarely been reported in patients with porokeratosis. We report an unusual case of linear porokeratosis at birth, with erosions and ulcerations of the face and lower extremity, that eluded diagnosis for nearly a year. Porokeratosis should be considered in the differential diagnosis of erosions in the newborn period.
汗孔角化症的典型表现为角质增厚的环状边缘向周围扩展,中心萎缩。线状汗孔角化症是一种变体,此类皮损呈线状排列,通常与皮节或Blaschko线相对应。汗孔角化症患者很少有溃疡的报道。我们报告了一例罕见的先天性线状汗孔角化症病例,患儿面部和下肢有糜烂和溃疡,近一年来一直未确诊。新生儿期糜烂的鉴别诊断应考虑汗孔角化症。