Livák F, Welsh S C, Guidos C J, Crispe I N, Danska J S, Schatz D G
Section of Immunobiology, Yale University School of Medicine, New Haven, Connecticut 06520, USA.
J Exp Med. 1996 Aug 1;184(2):419-28. doi: 10.1084/jem.184.2.419.
The developmental arrest of thymocytes from scid mice, deficient in variable, (diversity), and joining, or V(D)J recombination, can be overcome by sublethal gamma-irradiation. Since previous studies focused on restoration of rearrangement of the T cell receptor (TCR) beta locus, productive rearrangement of which is selected for, we sought to examine to what extent locus specificity and cellular selection contributed to the observed effects. We report here that irradiation of newborn scid mice induces normal V-D-J rearrangements of the TCR delta locus, which like TCR beta, is also actively rearranged in CD(4-)CD(8-) (double negative) thymocytes. In contrast, no complete V-J alpha rearrangements were detected. Instead, we detected substantial levels of hairpin-terminated coding ends at the 5' end of the J alpha locus, demonstrating that TCR alpha rearrangements manifest the effects of the scid mutation. Irradiation, therefore, transiently compensates for the effects of the scid mutation in a locus-nonspecific manner in thymocytes, resulting in a burst of normal TCR beta and delta rearrangements. Irradiation also allows the development of cells that can initiate but fail to complete V(D)J recombination events at the TCR alpha locus, which is normally inaccessible in scid thymocytes.
严重联合免疫缺陷(scid)小鼠的胸腺细胞因缺乏可变区、(多样性)区和连接区,即V(D)J重组而发育停滞,这种情况可通过亚致死剂量的γ射线照射得到克服。由于先前的研究集中在T细胞受体(TCR)β基因座重排的恢复上,而TCRβ基因座的有效重排是被选择的,我们试图研究基因座特异性和细胞选择在多大程度上导致了观察到的效应。我们在此报告,对新生scid小鼠进行照射可诱导TCRδ基因座正常的V-D-J重排,TCRδ基因座与TCRβ一样,也在CD(4-)CD(8-)(双阴性)胸腺细胞中活跃重排。相比之下,未检测到完整的V-Jα重排。相反,我们在Jα基因座的5'端检测到大量发夹末端编码末端,表明TCRα重排体现了scid突变的效应。因此,照射以基因座非特异性方式暂时补偿了胸腺细胞中scid突变的效应,导致正常的TCRβ和δ重排激增。照射还允许能够在TCRα基因座启动但未能完成V(D)J重组事件的细胞发育,而在scid胸腺细胞中,TCRα基因座通常是无法接近的。