Huang S F, Wu M H
Department of Pathology, College of Medicine, National Taiwan University, Taipei.
Heart. 1996 Jul;76(1):82-3. doi: 10.1136/hrt.76.1.82.
A female infant, born at 33 weeks' gestation with tetralogy of Fallot, died of severe perinatal asphyxia 6 hours after birth. Necropsy disclosed two associated vascular anomalies: a right aortic arch with a left common carotid artery arising from the pulmonary artery (isolated left common carotid artery) and an aberrant left subclavian artery arising from the descending aorta. Agenesis of the thymus and parathyroid gland was also found, suggesting that the child also had DiGeorge syndrome. Origin of the left common carotid artery from the pulmonary artery is exceedingly rare. When planning surgical treatment it is important to be aware of the possibility of this anomaly occurring in association with congenital heart disease, particularly in the presence of tetralogy of Fallot, right sided aortic arch, or DiGeorge syndrome.
一名孕33周出生的患有法洛四联症的女婴，出生后6小时死于严重围产期窒息。尸检发现两个相关的血管异常：右位主动脉弓，左颈总动脉发自肺动脉（孤立性左颈总动脉），以及左锁骨下动脉异常发自降主动脉。还发现胸腺和甲状旁腺发育不全，提示该患儿也患有迪格奥尔格综合征。左颈总动脉发自肺动脉极为罕见。在计划手术治疗时，重要的是要意识到这种异常可能与先天性心脏病相关，特别是在存在法洛四联症、右位主动脉弓或迪格奥尔格综合征的情况下。
