Hase T, Kodama M, Kishida A, Matsushita M, Kurumi Y, Mizukuro T, Okabe H, Uno M, Ohta S, Shimada M
First Department of Surgery, Shiga University of Medical Science, Japan.
J Pediatr Surg. 1995 Oct;30(10):1485-7. doi: 10.1016/0022-3468(95)90414-x.
A 4-month-old boy with benign hemangioma of the porta hepatis is described. Obstructive jaundice and consumption coagulopathy developed, which were treated by percutaneous transhepatic drainage (PTHD), without resection of the tumor or bypass surgery. Because of tumor regression, the patient has remained free of symptoms even after the PTHD tube was removed. Because juvenile hemangioma is a benign tumor and occasional spontaneous regression is known to occur (as in our case and other reports), it is suggested that complete resection or bypass surgery is not necessary for juvenile hemangioendothelioma, even with obstructive jaundice, if bile drainage is adequately maintained.
本文描述了一名患有肝门部良性血管瘤的4个月大男婴。该患儿出现了阻塞性黄疸和消耗性凝血病，通过经皮经肝引流术（PTHD）进行治疗，未进行肿瘤切除或旁路手术。由于肿瘤消退，即使在拔除PTHD管后，患者仍无症状。鉴于幼年型血管瘤是一种良性肿瘤，且已知偶尔会发生自发消退（如本例及其他报道），因此建议对于幼年型血管内皮瘤，即使伴有阻塞性黄疸，只要能充分维持胆汁引流，就无需进行完全切除或旁路手术。
