马凡综合征家族中晶状体异位的管理。
Management of ectopia lentis in a family with Marfan syndrome.
作者信息
Koenig S B, Mieler W F
机构信息
Department of Ophthalmology, Eye Institute, Medical College of Wisconsin, Milwaukee.
出版信息
Arch Ophthalmol. 1996 Sep;114(9):1058-61. doi: 10.1001/archopht.1996.01100140260001.
OBJECTIVE
To determine the effectiveness of combined pars plana vitrectomy-lensectomy and open-loop anterior chamber lens implantation for the management of ectopia lentis associated with Marfan syndrome.
METHODS
Retrospective review of the medical records of 4 consecutive patients with Marfan syndrome who underwent combined pars plana lensectomy-vitrectomy and anterior chamber lens implantation at our institution between August 1994 and July 1995.
RESULTS
All patients demonstrated postoperative visual acuity of 20/25 or better during an average follow-up period of 6 months (range, 4-9 months). Two patients developed pseudophakic pupillary block and required YAG laser iridotomy postoperatively.
CONCLUSIONS
Pars plana lensectomy-vitrectomy and anterior chamber intraocular lens implantation appears to be an excellent technique for the management of ectopia lentis associated with Marfan syndrome. A bimanual, closed-system endosurgical technique avoids many of the complications previously associated with surgery for ectopia lentis.
目的
确定玻璃体切割联合晶状体切除术及前房开放式人工晶状体植入术治疗马凡综合征相关晶状体异位的有效性。
方法
回顾性分析1994年8月至1995年7月在我院接受玻璃体切割联合晶状体切除术及前房人工晶状体植入术的4例连续性马凡综合征患者的病历资料。
结果
所有患者在平均6个月（4 - 9个月）的随访期内术后视力均达到20/25或更好。2例患者术后发生人工晶状体性瞳孔阻滞，需行YAG激光虹膜切开术。
结论
玻璃体切割联合晶状体切除术及前房人工晶状体植入术似乎是治疗马凡综合征相关晶状体异位的一种极佳技术。双手操作的闭合式内眼手术技术避免了许多先前与晶状体异位手术相关的并发症。
Zotero 插件