Franquet T, Giménez A, Cáceres J, Sabaté J M, Nadal C
Department of Diagnostic Radiology, Hospital de Sant Pau, Universidad Autónoma de Barcelona, Spain.
Radiographics. 1996 Jul;16(4):855-69. doi: 10.1148/radiographics.16.4.8835976.
Dermatologic lesions are often associated with pulmonary disorders and vice versa. Diseases with pulmonary and cutaneous manifestations can be divided into four major categories: (a) congenital and developmental disorders with cutaneous-pulmonary manifestations (Ehlers-Danlos syndrome, generalized elastolysis, yellow nail syndrome, neurofibromatosis, hereditary hemorrhagic telangiectasia); (b) primary dermal diseases with associated pulmonary manifestations (septic vasculitis, malignant melanoma, Kaposi sarcoma); (c) primary pulmonary diseases with associated cutaneous manifestations (tuberculosis, Pseudomonas pneumonia, mycoplasmal pneumonia, adenocarcinoma, metastasis); and (d) cutaneous-pulmonary conditions (multisystem disorders) (progressive systemic sclerosis, systemic lupus erythematosus, Wegener granulomatosis, sarcoidosis). A series of selected cases is used to illustrate the radiologic and dermatologic features of conditions that affect both the lung and dermal tissue. Specific emphasis is placed on the dermatologic manifestations of disease. Diagnosis of a pulmonary-cutaneous disorder requires familiarity with the morphologic appearance of the cutaneous lesion.
皮肤病变常与肺部疾病相关，反之亦然。有肺部和皮肤表现的疾病可分为四大类：(a) 伴有皮肤-肺部表现的先天性和发育性疾病（埃勒斯-当洛综合征、全身性弹性组织溶解症、黄甲综合征、神经纤维瘤病、遗传性出血性毛细血管扩张症）；(b) 伴有相关肺部表现的原发性皮肤病（感染性血管炎、恶性黑色素瘤、卡波西肉瘤）；(c) 伴有相关皮肤表现的原发性肺部疾病（结核病、铜绿假单胞菌肺炎、支原体肺炎、腺癌、转移瘤）；以及(d) 皮肤-肺部病症（多系统疾病）（进行性系统性硬化症、系统性红斑狼疮、韦格纳肉芽肿病、结节病）。通过一系列精选病例来说明影响肺部和皮肤组织的病症的放射学和皮肤学特征。特别强调疾病的皮肤表现。诊断肺-皮肤疾病需要熟悉皮肤病变的形态外观。
