Krauss J K, Jankovic J
Department of Neurosurgery, Baylor College of Medicine, Houston, Texas, USA.
Mov Disord. 1996 Sep;11(5):563-6. doi: 10.1002/mds.870110512.
We describe two patients with Tourette's syndrome in whom severe motor tics involving the neck were complicated by cervical myelopathy. The first patient, a 21-year-old man, had complex tics consisting of violent twisting and extending movements of the neck preceded by an irresistible urge to produce the abnormal postures. Two years after onset of these tics, paraesthesias, sensory deficits up to the level of C4, and a gait disturbance developed. Neuroimaging studies confirmed compressive myelopathy, and the symptoms gradually improved with botulinum toxin injections in the posterior cervical muscles. The second patient, a 42-year-old man, had violent clonic tics consisting of thrusting head jerks. The repetitive flexion-extension neck movements had been present since the age 10 years. At age 23, he developed progressive weakness of all four extremities and bladder and sexual dysfunction. Myelography demonstrated cervical spinal canal stenosis with retrospondylosis from C3 through C5 and a Klippel-Feil malformation. After cervical decompression by C3-C5 laminectomies, his spinal cord symptoms improved temporarily. The tics, however, continued, and the neurologic deficits of cervical myelopathy progressed again after age 34. He did not benefit from a second operation. This report draws attention to the possibility that some tics can produce disabling compressive myelopathy. Early diagnosis and treatment of the movement disorder is essential in such cases.
我们描述了两名患有妥瑞氏综合征的患者,他们颈部严重的运动性抽动并发了颈椎脊髓病。第一名患者是一名21岁男性,患有复杂的抽动症状,包括颈部剧烈扭转和伸展动作,在出现异常姿势之前有一种无法抗拒的冲动。这些抽动症状出现两年后,出现了感觉异常、C4水平以下的感觉缺陷以及步态障碍。神经影像学研究证实为压迫性脊髓病,通过在后颈部肌肉注射肉毒杆菌毒素,症状逐渐改善。第二名患者是一名42岁男性,患有剧烈的阵挛性抽动,表现为头部猛推抽搐。自10岁起就出现重复性的颈部屈伸运动。23岁时,他出现了四肢进行性无力以及膀胱和性功能障碍。脊髓造影显示颈椎管狭窄,伴有C3至C5的退变性脊椎病和Klippel-Feil畸形。在进行C3 - C5椎板切除术后颈椎减压,他的脊髓症状暂时改善。然而,抽动症状仍持续存在,34岁后颈椎脊髓病的神经功能缺损再次进展。他接受二次手术并未获益。本报告提请注意某些抽动可能导致致残性压迫性脊髓病的可能性。在此类病例中,对运动障碍进行早期诊断和治疗至关重要。