Tkebuchava T, von Segesser L K, Niederhäuser U, Bauersfeld U, Turina M
Clinic for Cardiovascular Surgery, University Hospital, Zurich, Switzerland.
Pediatr Cardiol. 1997 Jan-Feb;18(1):72-3. doi: 10.1007/s002469900115.
Two patients (one girl, one boy) with Kartagener syndrome (situs inversus, bronchiectasis, sinusitis), despite pulmonary problems and associated congenital cardiac anomalies, were operated on at the ages of 4 years and 7 years, respectively. They had had previous palliative treatment at the age of 3 months and 1.3 years, respectively. Both postoperative periods after total correction were without significant complications. Long-term follow-up was available for 9 and 19 years, respectively, with no manifestations of heart insufficiency. Both patients are physically active, and neither requires cardiac medication. Patients with Kartagener syndrome and associated congenital cardiac anomalies can successfully undergo multiple cardiac operations with good long-term outcome.
两名患有卡塔格内综合征(内脏反位、支气管扩张、鼻窦炎)的患者(一名女孩和一名男孩),尽管存在肺部问题及相关先天性心脏异常,但分别在4岁和7岁时接受了手术。他们此前分别在3个月和1.3岁时接受过姑息治疗。两次完全矫正手术后的恢复期均无严重并发症。分别有9年和19年的长期随访,均无心脏功能不全的表现。两名患者身体活动能力良好,均无需使用心脏药物。患有卡塔格内综合征及相关先天性心脏异常的患者能够成功接受多次心脏手术,并获得良好的长期预后。