Hanatate F, Matsuoka H, Mizuno Y, Kitamura T
National Shizuoka Hospital, Japan.
J Gastroenterol. 1995 Dec;30(6):786-9. doi: 10.1007/BF02349649.
A 59-year-old woman presented with consciousness disturbance with flapping tremor. Laboratory examinations revealed normal liver functions, and imaging studies, ultrasonography, magnetic resonance imaging, and angiography, showed portal vein aneurysm communicating from the portal vein to the hepatic vein, splenomegaly, and splenic artery aneurysm. These examinations confirmed porto-systemic shunt leading to hepatic encephalopathy. Porto-hepatic venous shunt via portal vein aneurysm is extremely rare, and there are few reports that it causes encephalopathy; therefore, little is known about the entity and this association. The literature in English is reviewed and the etiology, clinical features, and prognosis discussed.
一名59岁女性出现意识障碍伴扑翼样震颤。实验室检查显示肝功能正常，影像学检查，包括超声、磁共振成像和血管造影，显示门静脉瘤从门静脉通向肝静脉、脾肿大和脾动脉瘤。这些检查证实了导致肝性脑病的门体分流。通过门静脉瘤的门静脉-肝静脉分流极为罕见，很少有报道称其会导致脑病；因此，对这种情况及其关联知之甚少。本文回顾了英文文献并讨论了病因、临床特征和预后。
