Shormanov S V, Nikolaeva T N
Arkh Patol. 1977;39(5):67-9.
The article contains excerpts from case records and autopsy protocols for two children who had died of congenital valvular heart diseases. Both were full-term infants, with good weight who initially developed normally. During the first month of life, however, they developed respiratory disease which provoked the development of decompensation of the malformed heart. Moreover, both patients showed clinical signs of congestion not only in the greater circulation but in the lesser circulation as well. The latter was conditioned by anatomic features of the valvular defects. In the first case all the valves of the heart turned out to be malformed, in the second case there was observed a combination of Ebstein's anomaly with corrected transposition of the ventricles and major vessels of the heart and as a result the right ventricle with a malformed tricuspid valve was found to be on the place of the left ventricle.
本文包含两名死于先天性瓣膜性心脏病儿童的病例记录和尸检报告节选。两名均为足月儿,体重正常,最初发育正常。然而,在出生后的第一个月,他们患上了呼吸系统疾病,引发了畸形心脏失代偿的发展。此外,两名患者不仅在体循环中出现充血的临床症状,在肺循环中也出现了充血症状。后者是由瓣膜缺损的解剖特征决定的。在第一个病例中,心脏的所有瓣膜均出现畸形;在第二个病例中,观察到埃布斯坦畸形合并心脏心室和大血管的矫正型转位,结果发现右心室和畸形的三尖瓣位于左心室的位置。