Biliary tree rhabdomyosarcoma: report of one case.

A four-year-old boy was admitted due to abdominal distention for two years and jaundice of a few days duration. Abdominal ultrasound and CT scan of the abdomen showed marked dilatation of the common bile duct with two masses noted and a tumor extended to the left hepatic duct. Left hepatic lobectomy with Roux-en-Y right hepaticojejunostomy was performed which was histologically proved to be a embryonal type rhabdomyosarcoma. Chemotherapy was given postoperatively. The patient has had frequent follow-up for two years.