Huang J S, Chen C C, Wu Y M, Ho K Y, Wang C C, Ho Y P, Liu C S, Wang Y P
Department of Periodontology, School of Dentistry, Kaohsiung Medical College, Taiwan, Republic of China.
Kaohsiung J Med Sci. 1997 Feb;13(2):127-35.
Encephalotrigeminal angiomatosis (Sturge-Weber syndrome) is a rather uncommon congenital condition characterized by the combination of venous angioma of the leptomeninges over the cerebral cortex with ipsilateral angiomatous lesions of the face and sometimes, the skull, jaws and oral soft tissues. Two patients came to the Kaohsiung Medical College Hospital's dental clinic with complaints of localized gingival enlargement or tumor-like swelling. Based on the presence of facial nevus flammeus, examinations of angiography, radiological evidence of calcific densities, and ipsilaterally intraoral vascular hyperplasia in the lip, cheek and gingiva, encephalotrigeminal angiomatosis was diagnosed. Dental management included plaque control instructions, scaling, root planing and periodontal surgery. Recurrence of gingival enlargement in both cases was noted, so periodontal surgery was performed a second time. Close follow up and complete plaque control have kept the periodontal condition fairly well under control in these two cases. We introduce the oral manifestations and the experience of treatments in these two cases.
脑三叉神经血管瘤病（斯特奇-韦伯综合征）是一种相当罕见的先天性疾病，其特征是大脑皮质软脑膜静脉血管瘤与同侧面部血管瘤性病变相结合，有时还伴有颅骨、颌骨和口腔软组织病变。两名患者因局部牙龈肿大或肿瘤样肿胀前来高雄医学院医院牙科诊所就诊。基于面部葡萄酒色斑、血管造影检查、钙化密度的放射学证据以及同侧唇部、颊部和牙龈的口腔内血管增生，诊断为脑三叉神经血管瘤病。牙科治疗包括菌斑控制指导、洁治、根面平整和牙周手术。两例均出现牙龈肿大复发，因此再次进行了牙周手术。密切随访和完全的菌斑控制使这两例患者的牙周状况得到了较好的控制。我们介绍这两例患者的口腔表现及治疗经验。
