Manivannan Natarajan, Gokulanathan Subramanium, Ahathya Ramakrishnan Swamy, Daniel Rajkumar
Department of Oral and Maxillofacial Surgery, Vivekanandha Dental College for Women, Tiruchengode, India.
J Pharm Bioallied Sci. 2012 Aug;4(Suppl 2):S349-52. doi: 10.4103/0975-7406.100304.
Encephalotrigeminal angiomatosis (Sturge-Weber syndrome) is a rather uncommon congenital condition characterized by the combination of venous angioma of the leptomeninges over the cerebral cortex with ipsilateral angiomatous lesions of the face, and sometimes the skull, jaws, and oral soft tissues. A case of portwine stain with intraoral gingival hemangioma is presented. There were no other systemic manifestations. Patient reported with a complaint of localized tumor-like swelling in gums. Based on the presence of sharply demarcated vascular lesion unilaterally on the face and with ipsilateral intraoral vascular hyperplasia in the lip and gingiva, a variant of encephalotrigeminal angiomatosis was diagnosed. Ultrasound Doppler flowmetry was used to determine the blood flow. Dental management included plaque control instructions, scaling, root planning, and excision of the lesion done under general anesthesia. Close follow-up and meticulous plaque control have kept the oral condition under fairly good control.
脑三叉神经血管瘤病（斯特奇-韦伯综合征）是一种相当罕见的先天性疾病，其特征是大脑皮质软脑膜静脉血管瘤与同侧面部、有时还有颅骨、颌骨和口腔软组织的血管瘤样病变同时存在。本文报告一例伴有口腔内牙龈血管瘤的葡萄酒色斑病例。无其他全身表现。患者因牙龈局限性肿瘤样肿胀前来就诊。基于面部单侧边界清晰的血管病变以及同侧唇部和牙龈的口腔内血管增生，诊断为脑三叉神经血管瘤病的一种变异型。使用超声多普勒血流仪测定血流情况。牙科治疗包括菌斑控制指导、洗牙、根面平整以及在全身麻醉下切除病变。密切随访和细致的菌斑控制使口腔状况得到了较好的控制。
