原发性胆汁性肝硬化（PBC）-CREST重叠综合征合并干燥综合征
[Primary biliary cirrhosis (PBC)-CREST overlap syndrome complicated with Sjögren's syndrome].
作者信息
Akiyama Y, Suzuki T, Tanaka M, Fujimaki T, Asaoka T, Kobayashi K, Ohno S, Imai F, Matuo H
机构信息
Second Department of Internal Medicine, Saitama Medical School.
出版信息
Ryumachi. 1997 Feb;37(1):42-7.
PMID:9128423
Abstract
We reported two sisters of primary biliary cirrhosis (PBC)-CREST overlap syndrome complicated with Sjögren's syndrome (SS). Both patients had Raynaud's phenomenon, sclerodactylia, telangiectasia, chronic sialoadenitis, chronic nonsuppurative destructive cholangitis by liver biopsy and were positive for anti-centromere antibodies. This is the first report of two sisters of PBC-CREST overlap syndrome complicated with SS.
摘要
我们报告了两例原发性胆汁性肝硬化（PBC）-CREST重叠综合征合并干燥综合征（SS）的姐妹病例。两名患者均有雷诺现象、指端硬化、毛细血管扩张、慢性涎腺炎，肝活检显示慢性非化脓性破坏性胆管炎，且抗着丝点抗体均为阳性。这是首例关于两姐妹患有PBC-CREST重叠综合征合并SS的报告。
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