Segal A J, Spataro R F, Barbaric Z L
J Urol. 1977 Nov;118(5):711-3. doi: 10.1016/s0022-5347(17)58169-0.
Herein we review 100 cases of adult polycystic kidney disease. Flank pain was the most common presentation in these cases. In 20% of the patients calculi were noted and 10% had obstruction. The average patient age at death was 57 years. The importance of tomography is emphasized with key radiographic features, such as bilateral large kidneys, inhomogeneous nephrogram, caliceal distortion and poorly defined renal margins. Cystic involvement of the liver and spleen may help to confirm the diagnosis. Differential diagnosis includes bilateral multiple simple cysts, angiomyolipomatosis and bilateral renal carcinomas.
在此，我们回顾了100例成人多囊肾病患者的病例。胁腹痛是这些病例中最常见的症状。20%的患者发现有结石，10%的患者存在梗阻。患者的平均死亡年龄为57岁。强调了体层摄影术的重要性，其具有双侧大肾脏、肾图不均匀、肾盏变形和肾边缘模糊不清等关键影像学特征。肝脏和脾脏的囊性病变可能有助于确诊。鉴别诊断包括双侧多发性单纯囊肿、血管平滑肌脂肪瘤和双侧肾癌。
