给非输血依赖型重型地中海贫血患者输血的有益效果。
Beneficial effects of transfusing a patient with nontransfusion-dependent thalassaemia major.
作者信息
McIntosh N
出版信息
Arch Dis Child. 1976 Jun;51(6):471-2. doi: 10.1136/adc.51.6.471.
Abstract
A case of nontransfusion-dependent thalassaemia major is presented showing growth retardation, recurrent fractures, late onset of puberty, deafness, and endocrine impairment of pancreas and adrenal gland. Regular blood transfusion to maintain mean haemoglobin at about 11 g/de improvedd all these problems. It is suggested that this improvement was related to improve tissue oxygenation.
摘要
本文报告一例非输血依赖型重型地中海贫血病例，该病例表现出生长发育迟缓、反复骨折、青春期延迟、耳聋以及胰腺和肾上腺的内分泌功能损害。定期输血以维持平均血红蛋白水平在约11g/dL改善了所有这些问题。提示这种改善与组织氧合改善有关。
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