Oh K H, Ahn C, Park J H, Oh J E, Chin H J, Han J S, Kim S, Chi J G, Park M H, Lee J S
Department of Internal Medicine and Pathology, Seoul National University-Hospital, Korea.
Korean J Intern Med. 1997 Jun;12(2):232-7. doi: 10.3904/kjim.1997.12.2.232.
We present a 30-year-old male patient who was initially diagnosed as minimal change nephrotic syndrome, 5 years later, the patient developed a localized form of idiopathic retroperitoneal fibrosis (IRF). An elevated ESR and concomitant nephrotic syndrome in the patient suggested the immunologic nature of IRF, IRF has been reported in association with collagen diseases and rarely with proliferative and nonproliferative glomerulopathies. To our knowledge, the association between minimal change lesion (MC) and IRF has not been reported. Furthermore, the fact that IRF presented itself as an abdominal mass and lacked systemic symptoms was also unusual.
我们报告一名30岁男性患者，最初被诊断为微小病变型肾病综合征，5年后，该患者发展为局限性特发性腹膜后纤维化（IRF）。患者血沉升高并伴有肾病综合征，提示IRF的免疫性质，已有IRF与胶原病相关的报道，与增殖性和非增殖性肾小球病相关的报道则很少。据我们所知，微小病变（MC）与IRF之间的关联尚未见报道。此外，IRF表现为腹部肿块且无全身症状这一情况也不常见。
