Rouvillain J L, Jouannelle A, Delattre O, Pascal-Mousselard H, Catonne Y
Service de Chirurgie Orthopédique et Traumatologique, Fort-de-France, Martinique.
Rev Chir Orthop Reparatrice Appar Mot. 1997;83(4):372-7.
Chondromyxoid fibroma (CMF) is a very rare tumor. CMF represents less than 1p. 100 of all benign osseous tumors. The upper part of the tibia is the most frequent localization. We report the second case of talus tumor published in the world literature.
A 20 years old man presented a lytic tumor of the talus. The histology diagnosed a Chondromyxoid fibroma. A complete excision was made. An autologous bone graft associated with blocks of coral were used for reconstruction.
After six months sport activities were authorized. After 10 years follow-up, there is no recurrence, the coral has progressively disappeared, replaced by host bone.
Only one case of talus tumor has been published in world literature. Feldman has collected 189 cases of CMF published before 1970. After 1970, 297 new cases published. Analysis of these 486 cases pointed out the frequency of differents localizations.
This very rare tumor frequent between 10 and 30 years of age. The foot is the second localization after the tibia. A surgical conservative treatment with complete excision is recommended even in case of recurrence. Radiotherapy must be avoided in any case because of the risk of malignant degeneration.
软骨黏液样纤维瘤（CMF）是一种非常罕见的肿瘤。CMF在所有良性骨肿瘤中占比不到1%。胫骨上段是最常见的发病部位。我们报告了世界文献中第二例距骨肿瘤病例。
一名20岁男性出现距骨溶骨性肿瘤。组织学诊断为软骨黏液样纤维瘤。进行了完整切除。使用自体骨移植联合珊瑚块进行重建。
六个月后允许进行体育活动。经过10年随访，无复发，珊瑚块逐渐消失，被宿主骨替代。
世界文献中仅发表过一例距骨肿瘤病例。费尔德曼收集了1970年以前发表的189例CMF病例。1970年以后，又发表了297例新病例。对这486例病例的分析指出了不同发病部位的频率。
这种非常罕见的肿瘤常见于10至30岁之间。足部是仅次于胫骨的第二发病部位。即使复发，也建议采用完整切除的手术保守治疗。无论如何都必须避免放疗，因为有恶变风险。
