Genna M, Leopardi F, Fambri P, Postorino A
I Divisione Clinicizzata di Chirurgia Generale dell'Università di Verona.
Ann Ital Chir. 1997 May-Jun;68(3):351-3; discussion 353-4.
Neurilemmoma and Neurofibroma are benign tumours of the peripheral nerves that originate from the Schwann Cells. The finding of these tumours in the gastrointestinal tract in absence of generalized neurofibromatosis is uncommon and their presence in the anorectal area is extremely rare. From review of the literature we found only 34 cases of anorectal neurilemmoma. We report two patients, one with a rectal neurilemmoma and another with a perianal neurofibroma without a coexisting Von Recklinghausen's disease in either. In both cases they were asymptomatic and the surgical procedure performed was the simple tumorectomy which was diagnostic and curative. The literature on this subject is reviewed with particular attention to the possible malignant degeneration and the choice of the surgical approaches.
神经鞘瘤和神经纤维瘤是起源于施万细胞的周围神经良性肿瘤。在无全身性神经纤维瘤病的情况下，胃肠道出现这些肿瘤并不常见，而其出现在肛门直肠区域则极为罕见。通过文献回顾，我们仅发现34例肛门直肠神经鞘瘤病例。我们报告两例患者，一例为直肠神经鞘瘤，另一例为肛周神经纤维瘤，二者均无并存的冯·雷克林豪森病。两例患者均无症状，所施行的手术为单纯肿瘤切除术，兼具诊断和治愈作用。本文对该主题的文献进行了回顾，特别关注了可能的恶性变以及手术方式的选择。
